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Case Reports in Rheumatology
ISSN 2090-6897 · Wiley · 112 artikel di indeks
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Catastrophic Antiphospholipid Syndrome: A Rare but Life-Threatening Thrombotic Storm—A Case Report and Literature Review
Catastrophic antiphospholipid syndrome (CAPS) is a rare, life-threatening variant of antiphospholipid syndrome (APS) characterized by rapid, widespread thrombosis leading to multiorgan failure. Affecting less than 1% of APS patients, CAPS is associated with a high mortality rate of 30%–50%…
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A Diagnostic Pitfall: Lupus Mastitis Presenting Before Diagnosis of Systemic Lupus Erythematosus
Lupus erythematosus panniculitis or lupus erythematosus profundus (LEP) is a rare manifestation of cutaneous lupus erythematosus, with an estimated prevalence of 2%–3% in those with either systemic lupus erythematosus (SLE) or discoid lupus erythematosus (DLE). LEP with involvement of the breasts…
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A Case of Pseudogout in an Adolescent on Isotretinoin
Pseudogout or calcium pyrophosphate dihydrate deposition disease rarely occurs in the young. Known risk factors for pseudogout include age, previous surgery, trauma, metabolic conditions, and medications. Isotretinoin, a retinoid frequently used to control acne vulgaris, is known to cause…
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Dose-Escalated Upadacitinib for Refractory Myositis in Anti-Jo-1-Positive Antisynthetase Syndrome: A Case Report
Anti-Jo-1-positive antisynthetase syndrome (ASS) can follow a relapsing course during glucocorticoid tapering, and evidence for refractory myositis remains limited. We report a 33-year-old woman with anti-Jo-1-positive ASS with a dermatomyositis phenotype and recurrent myositis despite multiple…
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Successful Treatment of Anti-Jo-1 Positive Inflammatory Myopathy With Tofacitinib
Idiopathic inflammatory myopathies are, in some cases, refractory to all guideline-based treatments, posing a very difficult challenge in clinical practice. Janus kinase inhibitors are a rather new class of disease-modifying antirheumatic drugs that are approved for the treatment of rheumatoid…
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Case Report: Secukinumab Experience in a Patient With Coexistence of Systemic Lupus Erythematosus, Ankylosing Spondylitis, and Antiphospholipid Antibody Syndrome
Systemic lupus erythematosus (SLE) is a multisystem autoimmune disease characterized by autoantibody production and immune complex deposition. Antiphospholipid syndrome (APS) is frequently associated with SLE and is characterized by arterial or venous thrombosis and pregnancy morbidity in the…
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Crowned Dens Syndrome: A Case Report Describing Refractory Symptoms
Crowned dens syndrome (CDS) is a type of calcium pyrophosphate deposition disease that causes inflammation and pain due to calcium deposition in the odontoid process. Patients typically present with acute cervical pain often associated with fevers, elevated ESR and CRP, and leukocytosis. This…
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Overlap Myositis in a Patient With Psoriasis Treated With Anti–TNF-Alpha Therapy: A Case Report and Review of Literature
Overlap myositis refers to the simultaneous occurrence of myositis and another systemic autoimmune disease. Association between psoriasis and inflammatory myopathy is uncommon. Tumor necrosis factor (TNF)-alpha antagonists are used to treat patients with psoriasis and arthritis associated with…
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Childhood-Onset Takayasu Arteritis With Extensive Vascular Involvement: A Four-Decade Follow-Up Case Report
Childhood-onset Takayasu arteritis is rare, and data on outcomes beyond two or 3 decades are exceptionally limited. We report one of the longest documented follow-up observations of childhood-onset Takayasu arteritis, spanning more than 4 decades. The disease began at 9 years of age, and the…
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Navigating the Unknown: Scleroderma Renal Crisis and a Fatal Cardiac Complication in a Young Patient With MCTD With Coexisting Anti-U3 RNP and Anti-RNA Polymerase III Antibodies
We report the case of a 30-year-old Somali female with mixed connective tissue disease (MCTD) who developed dermatomyositis and both scleroderma renal crisis (SRC) and fatal cardiac complications. Notably, she tested positive for both anti-U3 RNP and anti-RNA polymerase III antibodies which is a…
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First-Line Tocilizumab Monotherapy for Juvenile Systemic Sclerosis With Interstitial Lung Disease: A Case Report
Systemic sclerosis, a rare autoimmune disease in children, frequently presents with aggressive clinical features and high risk of interstitial lung disease. Tocilizumab, an anti–interleukin-6 receptor monoclonal antibody, has exhibited efficacy in adult systemic sclerosis with interstitial lung…
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A Case of Critical Digit Ischemia in a Patient With Suspected Seronegative Scleroderma Diagnosed via Nailfold Capillaroscopy
Systemic sclerosis (scleroderma) can manifest with advanced symptoms of ischemic vasculopathy, including digital ulcer development. These ulcerations can be disabling and detrimental to a patient’s quality of life, so prompt diagnosis, differentiation from other vascular etiologies, and treatment…
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Recurrent Sterile Pleuropericarditis After Withdrawal of Renal Transplant Immunosuppression in Anuric ESRD: A Case of Suspected IL-1–Mediated Autoinflammation
Recurrent pericarditis and serositis pose a significant diagnostic challenge in patients with end-stage renal disease (ESRD) and a history of extensive immunosuppression. A 29-year-old man with anuric ESRD secondary to IgA nephropathy on intermittent hemodialysis, with a history of 2 failed kidney…
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Multierosive Juvenile Idiopathic Arthritis With Positive Rheumatoid Factor: A Case Report of a Young Girl Followed at the University Clinics of Bukavu
Polyarticular juvenile idiopathic arthritis (JIA) with positive rheumatoid factor is a rare and severe form of chronic inflammatory rheumatism in children. We report the case of a young girl treated at the University Clinics of Bukavu (eastern DR Congo), whose disease began at the age of 10. The…
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Use of Rituximab for Dermatomyositis Over Conventional Therapy: A Case Report
We present a case of a woman hospitalized with a known history of systemic lupus erythematosus (SLE) and Type 2 diabetes mellitus. She was referred from a local public district hospital in Richards Bay (KwaZulu-Natal, South Africa) to a tertiary/academic hospital, where her clinical assessment…
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Pericarditis as the Initial Manifestation of Antisynthetase Syndrome: A Case Report
Antisynthetase syndrome is a subtype of idiopathic inflammatory myopathy characterized by clinical manifestations that include myositis with a distinctive muscle biopsy pattern. Cardiac involvement has traditionally been considered a rare feature of this syndrome. Here, we report the case of a…
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Palmar Fasciitis and Polyarthritis With Erosive Disease: A Case Report
Palmar fasciitis and polyarthritis is a rare paraneoplastic syndrome that is nonerosive and associated with a high mortality rate. Metastatic undifferentiated epithelial carcinoma of unknown primary was diagnosed in a 59-year-old man who simultaneously developed palmar fasciitis and polyarthritis…
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Thymoma-Associated Systemic Lupus Erythematosus and Myasthenia Gravis
Thymomas, rare tumors originating from thymic epithelial cells, can disrupt immune tolerance and contribute to the development of autoimmune diseases. While thymomas are commonly associated with myasthenia gravis (MG), their link to autoimmune rheumatic diseases such as systemic lupus erythematosus…